July 2016

Transposition of the great arteries (TGA) is a congenital heart defect with ventriculoarterial discordance in which the aorta is aligned with the right ventricle and the pulmonary artery is aligned with the left ventricle. When atrioventricular (AV) concordance is present, this anatomy results in cyanosis because the systemic and pulmonary circulations are in parallel. The clinical diagnosis and management of patients with TGA has improved dramatically over the past three decades because of the evolution and availability of multiple imaging modalities and strides made in the surgical management of these patients. Despite these technical advances, patients with TGA require longterm surveillance because of ongoing anatomic and hemodynamic abnormalities. The purpose of this report is to present guidelines for multimodality imaging in this cohort of patients