March 2020

Congenital coronary artery anomalies, both in isolation and associated with other forms of congenital heart disease, have been recognized as important lesions with significant potential morbidity and mortality, including sudden cardiac death in children and adolescents. Multimodality imaging techniques have demonstrated increasing utility in the characterization of most congenital coronary anomalies, both in children and adults, and may reduce the need for diagnostic catheterization in many cases. This document provides multimodality guidelines for optimization of imaging for congenital coronary anomalies, with a review of the benefits and limitations of the different imaging techniques (echocardiography, cardiac computed tomography, cardiac magnetic resonance imaging, nuclear myocardial perfusion imaging and angiography).